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Sectoral retinitis pigmentosa

Sectoral retinitis pigmentosa is an autosomal dominant and usually associated with acceptable visual acuity. 

The fundus examination shows pigment clumps and chorioretinal atrophy only in sectoral with almost normal optic disc configuration and vessel diameter.

Fundus image showing Sectoral retinitis pigmentosa
Fundus image showing Sectoral retinitis pigmentosa


The sectoral retinitis pigmentosa symmetrical in both eyes
Perimetry will show scotoma corresponding to the dispersion of pigmentary clumps.

OCT shows outer retinal degeneration and RPE thining in the area of pigmentary clumps.

Please check Clinical guidelines in retinitis pigmentosa


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